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Selective Connexin43 Inhibition Prevents Isoproterenol-Induced Arrhythmias and Lethality in Muscular Dystrophy Mice

Duchenne muscular dystrophy (DMD) is caused by an X-linked mutation that leads to the absence of dystrophin, resulting in life-threatening arrhythmogenesis and associated heart failure. We targeted the gap junction protein connexin43 (Cx43) responsible for maintaining cardiac conduction. In mild mdx...

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Publicat a:Sci Rep
Autors principals: Patrick Gonzalez, J., Ramachandran, Jayalakshmi, Xie, Lai-Hua, Contreras, Jorge E., Fraidenraich, Diego
Format: Artigo
Idioma:Inglês
Publicat: Nature Publishing Group 2015
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4550874/
https://ncbi.nlm.nih.gov/pubmed/26311238
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/srep13490
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