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Activation of the Unfolded Protein Response in Sporadic Inclusion Body Myositis But Not in Hereditary GNE Inclusion Body Myopathy

Muscle fibers in patients with sporadic inclusion-body myositis (s-IBM), the most common age-associated myopathy, are characterized by autophagic vacuoles and accumulation of ubiquitinated and congophilic multiprotein aggregates that contain amyloid-β and phosphorylated tau. Muscle fibers of autosom...

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Dades bibliogràfiques
Publicat a:J Neuropathol Exp Neurol
Autors principals: Nogalska, Anna, D’Agostino, Carla, Engel, W. King, Cacciottolo, Mafalda, Asada, Shinichi, Mori, Kazutoshi, Askanas, Valerie
Format: Artigo
Idioma:Inglês
Publicat: 2015
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4506930/
https://ncbi.nlm.nih.gov/pubmed/25978849
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/NEN.0000000000000196
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