A carregar...

Antioxidant and anti-inflammatory agents mitigate pathology in a mouse model of pseudoachondroplasia

Pseudoachondroplasia (PSACH), a severe short-limb dwarfing condition, results from mutations that cause misfolding of the cartilage oligomeric matrix protein (COMP). Accumulated COMP in growth plate chondrocytes activates endoplasmic reticulum stress, leading to inflammation and chondrocyte death. U...

ver descrição completa

Na minha lista:
Detalhes bibliográficos
Publicado no:Hum Mol Genet
Main Authors: Posey, Karen L., Coustry, Francoise, Veerisetty, Alka C., Hossain, Mohammad, Alcorn, Joseph L., Hecht, Jacqueline T.
Formato: Artigo
Idioma:Inglês
Publicado em: Oxford University Press 2015
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4476442/
https://ncbi.nlm.nih.gov/pubmed/25859006
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/hmg/ddv122
Tags: Adicionar Tag
Sem tags, seja o primeiro a adicionar uma tag!