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Dysregulated Arginine Metabolism and Cardiopulmonary Dysfunction in Patients with Thalassaemia

Pulmonary hypertension (PH) commonly develops in thalassaemia syndromes, but is poorly characterized. The goal of this study was to provide a comprehensive description of the cardiopulmonary and biological profile of patients with thalassaemia at risk for PH. A case-control study of thalassaemia pat...

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Dades bibliogràfiques
Publicat a:Br J Haematol
Autors principals: Morris, Claudia R., Kim, Hae-Young, Klings, Elizabeth S., Wood, John, Porter, John B., Trachtenberg, Felicia, Sweeters, Nancy, Olivieri, Nancy F, Kwiatkowski, Janet L, Virzi, Lisa, Hassell, Kathryn, Taher, Ali, Neufeld, Ellis J, Thompson, Alexis A., Larkin, Sandra, Suh, Jung H., Vichinsky, Elliott P, Kuypers, Frans A.
Format: Artigo
Idioma:Inglês
Publicat: 2015
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4452408/
https://ncbi.nlm.nih.gov/pubmed/25907665
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1111/bjh.13452
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