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Bile Acid Pool Dynamics in Progressive Familial Intrahepatic Cholestasis with Partial External Bile Diversion

OBJECTIVES: Partial external bile diversion (PEBD) is an established therapy for low-GGT Progressive Familial Intrahepatic Cholestasis (PFIC). This study sought to determine if the dynamics of the cholic acid (CA) and chenodeoxycholic acid (CDCA) pools in low-GGT-PFIC subjects with successful PEBD w...

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Dettagli Bibliografici
Pubblicato in:J Pediatr Gastroenterol Nutr
Autori principali: Jericho, Hilary Smith, Kaurs, Elizabeth, Boverhof, Renze, Knisely, Alex, Shneider, Benjamin L, Verkade, Henkjan J, Whitington, Peter F
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2015
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4418648/
https://ncbi.nlm.nih.gov/pubmed/25383786
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/MPG.0000000000000630
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