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Odevixibat and partial external biliary diversion showed equal improvement of cholestasis in a patient with progressive familial intrahepatic cholestasis

Untreated progressive familial intrahepatic cholestasis (PFIC) type 2, or bile salt exporter protein deficiency, frequently leads to severe pruritus, impaired growth and progressive liver fibrosis with risk of organ failure. We describe a 15-month-old male patient with severe pruritus diagnosed with...

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Bibliografske podrobnosti
izdano v:BMJ Case Rep
Main Authors: Slavetinsky, Christoph, Sturm, Ekkehard
Format: Artigo
Jezik:Inglês
Izdano: BMJ Publishing Group 2020
Teme:
Online dostop:https://ncbi.nlm.nih.gov/pmc/articles/PMC7326258/
https://ncbi.nlm.nih.gov/pubmed/32601135
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/bcr-2019-234185
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