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A New CRB1 Rat Mutation Links Müller Glial Cells to Retinal Telangiectasia

We have identified and characterized a spontaneous Brown Norway from Janvier rat strain (BN-J) presenting a progressive retinal degeneration associated with early retinal telangiectasia, neuronal alterations, and loss of retinal Müller glial cells resembling human macular telangiectasia type 2 (MacT...

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Detalhes bibliográficos
Publicado no:J Neurosci
Main Authors: Zhao, Min, Andrieu-Soler, Charlotte, Kowalczuk, Laura, Paz Cortés, María, Berdugo, Marianne, Dernigoghossian, Marilyn, Halili, Francisco, Jeanny, Jean-Claude, Goldenberg, Brigitte, Savoldelli, Michèle, El Sanharawi, Mohamed, Naud, Marie-Christine, van Ijcken, Wilfred, Pescini-Gobert, Rosanna, Martinet, Danielle, Maass, Alejandro, Wijnholds, Jan, Crisanti, Patricia, Rivolta, Carlo, Behar-Cohen, Francine
Formato: Artigo
Idioma:Inglês
Publicado em: Society for Neuroscience 2015
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4397606/
https://ncbi.nlm.nih.gov/pubmed/25878282
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1523/JNEUROSCI.3412-14.2015
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