Chargement en cours...
Cystinotic fibroblasts accumulate cystine from intracellular protein degradation.
Fibroblasts derived from patients with cystinosis, an autosomal recessive condition, accumulate the disulfide amino acid cystine within lysosomes. The metabolic defect leading to the cystine accumulation and the source from which the cystine is derived are unknown. In this report we present data sho...
Enregistré dans:
| Auteurs principaux: | , , , |
|---|---|
| Format: | Artigo |
| Langue: | Inglês |
| Publié: |
1977
|
| Sujets: | |
| Accès en ligne: | https://ncbi.nlm.nih.gov/pmc/articles/PMC431972/ https://ncbi.nlm.nih.gov/pubmed/270698 |
| Tags: |
Ajouter un tag
Pas de tags, Soyez le premier à ajouter un tag!
|