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A Plakophilin-1 Gene Mutation in an Egyptian Family with Ectodermal Dysplasia-Skin Fragility Syndrome

Ectodermal dysplasia-skin fragility syndrome (ED-SFS) is a rare genodermatosis caused by mutations in the PKP1 gene, encoding the desmosomal plaque protein plakophilin-1. Since its initial description in 1997, few individuals with this disorder have been reported to date. Here, we present the first...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Argitaratua izan da:Mol Syndromol
Egile Nagusiak: Abdalla, Ebtesam M., Has, Cristina
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: S. Karger AG 2014
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC4281574/
https://ncbi.nlm.nih.gov/pubmed/25565931
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1159/000369267
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