Caricamento...

Dihydropyrimidine Dehydrogenase Deficiency in Two Malaysian Siblings with Abnormal MRI Findings

Dihydropyrimidine dehydrogenase (DPD) deficiency is an autosomal recessive disorder of the pyrimidine metabolism. Deficiency of this enzyme leads to an accumulation of thymine and uracil and a deficiency of metabolites distal to the catabolic enzyme. The disorder presents with a wide clinical spectr...

Descrizione completa

Salvato in:
Dettagli Bibliografici
Pubblicato in:Mol Syndromol
Autori principali: Chen, Bee Chin, Mohd Rawi, Rowani, Meinsma, Rutger, Meijer, Judith, Hennekam, Raoul C.M., van Kuilenburg, André B.P.
Natura: Artigo
Lingua:Inglês
Pubblicazione: S. Karger AG 2014
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4281573/
https://ncbi.nlm.nih.gov/pubmed/25565930
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1159/000366074
Tags: Aggiungi Tag
Nessun Tag, puoi essere il primo ad aggiungerne! !