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Facioscapulohumeral Muscular Dystrophy: More Complex than it Appears

Facioscapulohumeral muscular dystrophy (FSHD) has been classified as an autosomal dominant myopathy, linked to rearrangements in an array of 3.3 kb tandemly repeated DNA elements (D4Z4) located at the 4q subtelomere (4q35). For the last 20 years, the diagnosis of FSHD has been confirmed in clinical...

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Dades bibliogràfiques
Publicat a:Curr Mol Med
Autors principals: G, Ricci, M, Zatz, R, Tupler
Format: Artigo
Idioma:Inglês
Publicat: Bentham Science Publishers 2014
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4264243/
https://ncbi.nlm.nih.gov/pubmed/25323867
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.2174/1566524014666141010155054
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