Yüklüyor......

Improvement of Cardiomyopathy After High-Fat Diet in Two Siblings with Glycogen Storage Disease Type III

Glycogenosis type III (GSD III) is an autosomal recessive disorder due to amylo-1,6-glucosidase deficiency. This disease causes limit dextrin storage in affected tissues: liver, skeletal muscles, and heart in GSD IIIa and only liver in GSD IIIb. Cardiomyopathy is quite frequent in GSD IIIa with vari...

Ful tanımlama

Kaydedildi:
Detaylı Bibliyografya
Yayımlandı:JIMD Rep
Asıl Yazarlar: Brambilla, Alessandra, Mannarino, Savina, Pretese, Roberta, Gasperini, Serena, Galimberti, Cinzia, Parini, Rossella
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: Springer Berlin Heidelberg 2014
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC4241197/
https://ncbi.nlm.nih.gov/pubmed/25308556
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/8904_2014_343
Etiketler: Etiketle
Etiket eklenmemiş, İlk siz ekleyin!