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Glycogen storage disease type III: modified Atkins diet improves myopathy

BACKGROUND: Frequent feeds with carbohydrate-rich meals or continuous enteral feeding has been the therapy of choice in glycogen storage disease (Glycogenosis) type III. Recent guidelines on diagnosis and management recommend frequent feedings with high complex carbohydrates or cornstarch avoiding f...

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Dades bibliogràfiques
Publicat a:Orphanet J Rare Dis
Autors principals: Mayorandan, Sebene, Meyer, Uta, Hartmann, Hans, Das, Anibh Martin
Format: Artigo
Idioma:Inglês
Publicat: BioMed Central 2014
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4302571/
https://ncbi.nlm.nih.gov/pubmed/25431232
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13023-014-0196-3
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