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Congenital deficiency of two polypeptide subunits of the iron-protein fragment of mitochondrial complex I.

Recently, we described a patient with severe lactic acidosis due to congenital complex I (NADH-ubiquinone oxidoreductase) deficiency. We now report further enzymatic and immunological characterizations. Both NADH and ferricyanide titrations of complex I activity (measured as NADH-ferricyanide reduct...

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Dettagli Bibliografici
Pubblicato in:J Clin Invest
Autori principali: Moreadith, R W, Cleeter, M W, Ragan, C I, Batshaw, M L, Lehninger, A L
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Society for Clinical Investigation 1987
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Accesso online:https://ncbi.nlm.nih.govhttps://pmc.ncbi.nlm.nih.gov/articles/PMC424102/
https://ncbi.nlm.nih.govhttps://pubmed.ncbi.nlm.nih.gov/3100577/
https://ncbi.nlm.nih.govhttps://doi.org/10.1172/JCI112834
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