Congenital deficiency of two polypeptide subunits of the iron-protein fragment of mitochondrial complex I.

Recently, we described a patient with severe lactic acidosis due to congenital complex I (NADH-ubiquinone oxidoreductase) deficiency. We now report further enzymatic and immunological characterizations. Both NADH and ferricyanide titrations of complex I activity (measured as NADH-ferricyanide reduct...

Descripción completa

Guardado en:
Detalles Bibliográficos
Autores principales: Moreadith, R W, Cleeter, M W, Ragan, C I, Batshaw, M L, Lehninger, A L
Formato: Artigo
Lenguaje:Inglês
Publicado: 1987
Materias:
Research Article
Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC424102/
https://ncbi.nlm.nih.gov/pubmed/3100577
Etiquetas: Agregar Etiqueta
Sin Etiquetas, Sea el primero en etiquetar este registro!

Ejemplares similares