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Constitutive expression of Gsα(R201C) in mice produces a heritable, direct replica of human fibrous dysplasia bone pathology and demonstrates its natural history

Fibrous dysplasia of bone (FD) is a crippling skeletal disease associated with post zygotic mutations (R201C, R201H) of the gene encoding the α subunit of the stimulatory G protein, Gs. By causing a characteristic structural subversion of bone and bone marrow, the disease results in deformity, hypom...

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Dettagli Bibliografici
Autori principali: Saggio, Isabella, Remoli, Cristina, Spica, Emanuela, Cersosimo, Stefania, Sacchetti, Benedetto, Robey, Pamela G., Holmbeck, Kenn, Cumano, Ana, Boyde, Alan, Bianco, Paolo, Riminucci, Mara
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2014
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4205271/
https://ncbi.nlm.nih.gov/pubmed/24764158
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/jbmr.2267
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