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Myogenesis in dysferlin-deficient myoblasts is inhibited by an intrinsic inflammatory response
Limb-girdle muscular dystrophy type 2B results from mutations in dysferlin, a membrane-associated protein involved in cellular membrane repair. Primary myoblast cultures derived from dysferlinopathy patients show reduced myogenic potential, suggesting that dysferlin may regulate myotube fusion and b...
Tallennettuna:
Päätekijät: | , , |
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Aineistotyyppi: | Artigo |
Kieli: | Inglês |
Julkaistu: |
2012
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Aiheet: | |
Linkit: | https://ncbi.nlm.nih.gov/pmc/articles/PMC4147957/ https://ncbi.nlm.nih.gov/pubmed/22560623 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.nmd.2012.03.002 |
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