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Myogenesis in dysferlin-deficient myoblasts is inhibited by an intrinsic inflammatory response

Limb-girdle muscular dystrophy type 2B results from mutations in dysferlin, a membrane-associated protein involved in cellular membrane repair. Primary myoblast cultures derived from dysferlinopathy patients show reduced myogenic potential, suggesting that dysferlin may regulate myotube fusion and b...

Täydet tiedot

Tallennettuna:
Bibliografiset tiedot
Päätekijät: Cohen, Tatiana V., Cohen, Jonathan E., Partridge, Terence A.
Aineistotyyppi: Artigo
Kieli:Inglês
Julkaistu: 2012
Aiheet:
Linkit:https://ncbi.nlm.nih.gov/pmc/articles/PMC4147957/
https://ncbi.nlm.nih.gov/pubmed/22560623
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.nmd.2012.03.002
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