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Three charged amino acids in extracellular loop 1 are involved in maintaining the outer pore architecture of CFTR

The cystic fibrosis (CF) transmembrane conductance regulator (CFTR) bears six extracellular loops (ECL1–6); ECL1 is the site of several mutations associated with CF. Mutation R117H has been reported to reduce current amplitude, whereas D110H, E116K, and R117C/L/P may impair channel stability. We hyp...

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Dettagli Bibliografici
Autori principali: Cui, Guiying, Rahman, Kazi S., Infield, Daniel T., Kuang, Christopher, Prince, Chengyu Z., McCarty, Nael A.
Natura: Artigo
Lingua:Inglês
Pubblicazione: The Rockefeller University Press 2014
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4113900/
https://ncbi.nlm.nih.gov/pubmed/25024266
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1085/jgp.201311122
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