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Abnormal n-6 fatty acid metabolism in cystic fibrosis is caused by activation of AMP-activated protein kinase

Cystic fibrosis (CF) patients and model systems exhibit consistent abnormalities in PUFA metabolism, including increased metabolism of linoleate to arachidonate. Recent studies have connected these abnormalities to increased expression and activity of the Δ6- and Δ5-desaturase enzymes. However, the...

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Autors principals: Umunakwe, Obi C., Seegmiller, Adam C.
Format: Artigo
Idioma:Inglês
Publicat: The American Society for Biochemistry and Molecular Biology 2014
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4076094/
https://ncbi.nlm.nih.gov/pubmed/24859760
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1194/jlr.M050369
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