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Protein Stability, Folding and Misfolding in Human PGK1 Deficiency

Conformational diseases are often caused by mutations, altering protein folding and stability in vivo. We review here our recent work on the effects of mutations on the human phosphoglycerate kinase 1 (hPGK1), with a particular focus on thermodynamics and kinetics of protein folding and misfolding....

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Bibliografski detalji
Glavni autori: Valentini, Giovanna, Maggi, Maristella, Pey, Angel L.
Format: Artigo
Jezik:Inglês
Izdano: MDPI 2013
Teme:
Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC4030965/
https://ncbi.nlm.nih.gov/pubmed/24970202
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/biom3041030
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