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Progressive Familial Intrahepatic Cholestasis

Progressive familial intrahepatic cholestasis (PFIC) is a group of rare disorders which are caused by defect in bile secretion and present with intrahepatic cholestasis, usually in infancy and childhood. These are autosomal recessive in inheritance. The estimated incidence is about 1 per 50,000 to 1...

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Dettagli Bibliografici
Autore principale: Srivastava, Anshu
Natura: Artigo
Lingua:Inglês
Pubblicazione: Elsevier 2014
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4017198/
https://ncbi.nlm.nih.gov/pubmed/25755532
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.jceh.2013.10.005
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