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Progressive Familial Intrahepatic Cholestasis

Progressive familial intrahepatic cholestasis (PFIC) is a group of rare disorders which are caused by defect in bile secretion and present with intrahepatic cholestasis, usually in infancy and childhood. These are autosomal recessive in inheritance. The estimated incidence is about 1 per 50,000 to 1...

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Библиографические подробности
Главный автор: Srivastava, Anshu
Формат: Artigo
Язык:Inglês
Опубликовано: Elsevier 2014
Предметы:
Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC4017198/
https://ncbi.nlm.nih.gov/pubmed/25755532
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.jceh.2013.10.005
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