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Progressive Familial Intrahepatic Cholestasis

Progressive familial intrahepatic cholestasis (PFIC) is a group of rare disorders which are caused by defect in bile secretion and present with intrahepatic cholestasis, usually in infancy and childhood. These are autosomal recessive in inheritance. The estimated incidence is about 1 per 50,000 to 1...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Egile nagusia: Srivastava, Anshu
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: Elsevier 2014
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC4017198/
https://ncbi.nlm.nih.gov/pubmed/25755532
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.jceh.2013.10.005
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