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Glanzmann Thrombasthenia: State of the Art and Future Directions

Glanzmann thrombasthenia (GT) is the principal inherited disease of platelets and the most commonly encountered disorder of an integrin. GT is characterized by spontaneous mucocutaneous bleeding and an exaggerated response to trauma due to platelets that fail to aggregate when stimulated by physiolo...

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Autores principales: Nurden, Alan T, Pillois, Xavier, Wilcox, David A.
Formato: Artigo
Lenguaje:Inglês
Publicado: 2013
Materias:
Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC4011384/
https://ncbi.nlm.nih.gov/pubmed/23929305
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1055/s-0033-1353393
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