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Pathophysiology of childhood polycystic kidney diseases: new insights into disease-specific therapy

ADPKD and ARPKD are a significant cause of morbidity and mortality in children and young adults. ADPKD with an incidence of 1:400–1,000 affects over 13 million individuals worldwide, and is a major cause of end-stage renal disease (ESRD) in adults. However, symptomatic disease is increasingly recogn...

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Autori principali: Sweeney, William E., Avner, Ellis D.
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2013
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3953890/
https://ncbi.nlm.nih.gov/pubmed/24336431
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/pr.2013.191
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