Загрузка...

Effect of vanillic acid on COQ6 mutants identified in patients with coenzyme Q(10) deficiency()

Human COQ6 encodes a monooxygenase which is responsible for the C5-hydroxylation of the quinone ring of coenzyme Q (CoQ). Mutations in COQ6 cause primary CoQ deficiency, a condition responsive to oral CoQ(10) supplementation. Treatment is however still problematic given the poor bioavailability of C...

Полное описание

Сохранить в:
Библиографические подробности
Главные авторы: Doimo, Mara, Trevisson, Eva, Airik, Rannar, Bergdoll, Marc, Santos-Ocaña, Carlos, Hildebrandt, Friedhelm, Navas, Placido, Pierrel, Fabien, Salviati, Leonardo
Формат: Artigo
Язык:Inglês
Опубликовано: Elsevier Pub. Co 2014
Предметы:
Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC3898990/
https://ncbi.nlm.nih.gov/pubmed/24140869
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.bbadis.2013.10.007
Метки: Добавить метку
Нет меток, Требуется 1-ая метка записи!