Llwytho...

Molecular and Clinical Investigation of Iranian Patients with Friedreich Ataxia

Background: Friedreich ataxia (FRDA) is an autosomal recessive disorder caused by guanine-adenine-adenine (GAA) triplet expansions in the FXN gene. Its product, frataxin, which severely reduces in FRDA patients, leads to oxidative damage in mitochondria. The purpose of this study was to evaluate the...

Disgrifiad llawn

Wedi'i Gadw mewn:
Manylion Llyfryddiaeth
Prif Awduron: Salehi, Mohammad Hossein, Houshmand, Massoud, Aryani, Omid, Kamalidehghan, Behnam, Khalili, Elham
Fformat: Artigo
Iaith:Inglês
Cyhoeddwyd: Pasteur Institute of Iran 2014
Pynciau:
Mynediad Ar-lein:https://ncbi.nlm.nih.gov/pmc/articles/PMC3892137/
https://ncbi.nlm.nih.gov/pubmed/24375160
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.6091/ibj.1235.2013
Tagiau: Ychwanegu Tag
Dim Tagiau, Byddwch y cyntaf i dagio'r cofnod hwn!