Á lódáil...

Molecular and Clinical Investigation of Iranian Patients with Friedreich Ataxia

Background: Friedreich ataxia (FRDA) is an autosomal recessive disorder caused by guanine-adenine-adenine (GAA) triplet expansions in the FXN gene. Its product, frataxin, which severely reduces in FRDA patients, leads to oxidative damage in mitochondria. The purpose of this study was to evaluate the...

Cur síos iomlán

Na minha lista:
Sonraí Bibleagrafaíochta
Main Authors: Salehi, Mohammad Hossein, Houshmand, Massoud, Aryani, Omid, Kamalidehghan, Behnam, Khalili, Elham
Formáid: Artigo
Teanga:Inglês
Foilsithe: Pasteur Institute of Iran 2014
Ábhair:
Rochtain Ar Líne:https://ncbi.nlm.nih.gov/pmc/articles/PMC3892137/
https://ncbi.nlm.nih.gov/pubmed/24375160
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.6091/ibj.1235.2013
Clibeanna: Cuir Clib Leis
Gan Chlibeanna, Bí ar an gcéad duine leis an taifead seo a chlibeáil!