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Mitochondrial respiration without ubiquinone biosynthesis

Ubiquinone (UQ), a.k.a. coenzyme Q, is a redox-active lipid that participates in several cellular processes, in particular mitochondrial electron transport. Primary UQ deficiency is a rare but severely debilitating condition. Mclk1 (a.k.a. Coq7) encodes a conserved mitochondrial enzyme that is neces...

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Autori principali: Wang, Ying, Hekimi, Siegfried
Natura: Artigo
Lingua:Inglês
Pubblicazione: Oxford University Press 2013
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3888124/
https://ncbi.nlm.nih.gov/pubmed/23847050
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/hmg/ddt330
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