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Pupillary Light Reflex Deficits in a Canine Model of Late Infantile Neuronal Ceroid Lipofuscinosis

Late-infantile neuronal ceroid lipofuscinosis (CLN2) is a hereditary neurological disorder characterized by progressive retinal degeneration and vision loss, cognitive and motor decline, seizures, and pronounced brain atrophy. The progressive loss of neurological functions eventually leads to death,...

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Detalles Bibliográficos
Main Authors: Whiting, Rebecca E.H., Narfström, Kristina, Yao, Gang, Pearce, Jacqueline W., Coates, Joan R., Castaner, Leilani J., Katz, Martin L.
Formato: Artigo
Idioma:Inglês
Publicado: 2013
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC3845481/
https://ncbi.nlm.nih.gov/pubmed/24135299
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.exer.2013.10.006
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