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Hypersensitivity of excitation-contraction coupling in dystrophic cardiomyocytes

Duchenne muscular dystrophy represents a severe inherited disease of striated muscle. It is caused by a mutation of the dystrophin gene and characterized by a progressive loss of skeletal muscle function. Most patients also develop a dystrophic cardiomyopathy, resulting in dilated hypertrophy and he...

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Autors principals: Ullrich, Nina D., Fanchaouy, Mohammed, Gusev, Konstantin, Shirokova, Natalia, Niggli, Ernst
Format: Artigo
Idioma:Inglês
Publicat: American Physiological Society 2009
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3774091/
https://ncbi.nlm.nih.gov/pubmed/19783774
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1152/ajpheart.00602.2009
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