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Tissue-specific effects of saposin A and saposin B on glycosphingolipid degradation in mutant mice

Individual saposin A (A−/−) and saposin B (B−/−)-deficient mice show unique phenotypes caused by insufficient degradation of myelin-related glycosphingolipids (GSLs): galactosylceramide and galactosylsphingosine and sulfatide, respectively. To gain insight into the interrelated functions of saposins...

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Bibliografiske detaljer
Main Authors: Sun, Ying, Zamzow, Matt, Ran, Huimin, Zhang, Wujuan, Quinn, Brian, Barnes, Sonya, Witte, David P., Setchell, Kenneth D.R., Williams, Michael T., Vorhees, Charles V., Grabowski, Gregory A.
Format: Artigo
Sprog:Inglês
Udgivet: Oxford University Press 2013
Fag:
Online adgang:https://ncbi.nlm.nih.gov/pmc/articles/PMC3708521/
https://ncbi.nlm.nih.gov/pubmed/23446636
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/hmg/ddt096
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