Cargando...

Proteasome overload is a common stress factor in multiple forms of inherited retinal degeneration

Inherited retinal degenerations, caused by mutations in over 100 individual genes, affect approximately 2 million people worldwide. Many of the underlying mutations cause protein misfolding or mistargeting in affected photoreceptors. This places an increased burden on the protein folding and degrada...

Descrición completa

Gardado en:
Detalles Bibliográficos
Main Authors: Lobanova, Ekaterina S., Finkelstein, Stella, Skiba, Nikolai P., Arshavsky, Vadim Y.
Formato: Artigo
Idioma:Inglês
Publicado: National Academy of Sciences 2013
Assuntos:
Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC3683722/
https://ncbi.nlm.nih.gov/pubmed/23716657
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.1305521110
Tags: Engadir etiqueta
Sen Etiquetas, Sexa o primeiro en etiquetar este rexistro!