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Proteasome overload is a common stress factor in multiple forms of inherited retinal degeneration

Inherited retinal degenerations, caused by mutations in over 100 individual genes, affect approximately 2 million people worldwide. Many of the underlying mutations cause protein misfolding or mistargeting in affected photoreceptors. This places an increased burden on the protein folding and degrada...

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Autori principali: Lobanova, Ekaterina S., Finkelstein, Stella, Skiba, Nikolai P., Arshavsky, Vadim Y.
Natura: Artigo
Lingua:Inglês
Pubblicazione: National Academy of Sciences 2013
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3683722/
https://ncbi.nlm.nih.gov/pubmed/23716657
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.1305521110
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