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Pyridostigmine but not 3,4-diaminopyridine exacerbates ACh receptor loss and myasthenia induced in mice by muscle-specific kinase autoantibody

In myasthenia gravis, the neuromuscular junction is impaired by the antibody-mediated loss of postsynaptic acetylcholine receptors (AChRs). Muscle weakness can be improved upon treatment with pyridostigmine, a cholinesterase inhibitor, or with 3,4-diaminopyridine, which increases the release of ACh...

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Autors principals: Morsch, Marco, Reddel, Stephen W, Ghazanfari, Nazanin, Toyka, Klaus V, Phillips, William D
Format: Artigo
Idioma:Inglês
Publicat: Blackwell Science Inc 2013
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3678053/
https://ncbi.nlm.nih.gov/pubmed/23440963
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1113/jphysiol.2013.251827
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