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FUS regulates genes coding for RNA-binding proteins in neurons by binding to their highly conserved introns

Dominant mutations and mislocalization or aggregation of Fused in Sarcoma (FUS), an RNA-binding protein (RBP), cause neuronal degeneration in Amyotrophic Lateral Sclerosis (ALS) and Frontotemporal Lobar Degeneration (FTLD), two incurable neurological diseases. However, the function of FUS in neurons...

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Main Authors: Nakaya, Tadashi, Alexiou, Panagiotis, Maragkakis, Manolis, Chang, Alexandra, Mourelatos, Zissimos
Formato: Artigo
Idioma:Inglês
Publicado: Cold Spring Harbor Laboratory Press 2013
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC3677260/
https://ncbi.nlm.nih.gov/pubmed/23389473
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1261/rna.037804.112
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