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TFEB-mediated autophagy rescues midbrain dopamine neurons from α-synuclein toxicity

The aggregation of α-synuclein plays a major role in Parkinson disease (PD) pathogenesis. Recent evidence suggests that defects in the autophagy-mediated clearance of α-synuclein contribute to the progressive loss of nigral dopamine neurons. Using an in vivo model of α-synuclein toxicity, we show th...

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Autores principales: Decressac, Mickael, Mattsson, Bengt, Weikop, Pia, Lundblad, Martin, Jakobsson, Johan, Björklund, Anders
Formato: Artigo
Lenguaje:Inglês
Publicado: National Academy of Sciences 2013
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC3651458/
https://ncbi.nlm.nih.gov/pubmed/23610405
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.1305623110
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