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A 1.3-Mb 7q11.23 Atypical Deletion Identified in a Cohort of Patients with Williams-Beuren Syndrome

Williams-Beuren syndrome is a rare multisystem neurodevelopmental disorder caused by a 1.55-1.84-Mb hemizygous deletion on chromosome 7q11.23. The classical phenotype consists of characteristic facial features, supravalvular aortic stenosis, intellectual disability, overfriendliness, and visuospatia...

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Autori principali: Delgado, L.M., Gutierrez, M., Augello, B., Fusco, C., Micale, L., Merla, G., Pastene, E.A.
Natura: Artigo
Lingua:Inglês
Pubblicazione: S. Karger AG 2013
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3638923/
https://ncbi.nlm.nih.gov/pubmed/23653586
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1159/000347167
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