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Protease-sensitive prions with 144-bp insertion mutations

Insertion of 144-base pair (bp) containing six extra octapeptide repeats between residues 51 and 91 of prion protein (PrP) gene is associated with inherited prion diseases. Most cases linked to this insertion examined by Western blotting showed detectable proteinase K-resistant PrP(Sc) (rPrP(Sc)) re...

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Detaylı Bibliyografya
Asıl Yazarlar: Xiao, Xiangzhu, Cali, Ignazio, Dong, Zhiqian, Puoti, Gianfranco, Yuan, Jue, Qing, Liuting, Wang, Heming, Kong, Qingzhong, Gambetti, Pierluigi, Zou, Wen-Quan
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: Impact Journals LLC 2013
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC3629288/
https://ncbi.nlm.nih.gov/pubmed/23515139
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