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Berardinelli–Seip syndrome: highlight of treatment challenge

Berardinelli–Seip congenital lipodystrophy (BSCL) syndrome is a rare autosomal-recessive disease characterised by lipoatrophy and associated with deregulations of glycidic and lipid metabolism. We report three BSCL cases with its typical clinical picture and complications. Clinically, they all show...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Egile Nagusiak: Ferraria, Nélia, Pedrosa, Cristina, Amaral, Daniela, Lopes, Lurdes
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: BMJ Publishing Group 2013
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC3604279/
https://ncbi.nlm.nih.gov/pubmed/23362058
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/bcr-2012-007734
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