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Berardinelli–Seip syndrome: highlight of treatment challenge

Berardinelli–Seip congenital lipodystrophy (BSCL) syndrome is a rare autosomal-recessive disease characterised by lipoatrophy and associated with deregulations of glycidic and lipid metabolism. We report three BSCL cases with its typical clinical picture and complications. Clinically, they all show...

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Autors principals: Ferraria, Nélia, Pedrosa, Cristina, Amaral, Daniela, Lopes, Lurdes
Format: Artigo
Idioma:Inglês
Publicat: BMJ Publishing Group 2013
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3604279/
https://ncbi.nlm.nih.gov/pubmed/23362058
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/bcr-2012-007734
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