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Gastric Cancer in Individuals with Li-Fraumeni Syndrome

PURPOSE: Li-Fraumeni Syndrome (LFS) is a rare hereditary cancer syndrome associated with germline mutations in the TP53 gene. While sarcomas, brain tumors, leukemias, breast and adrenal cortical carcinomas are typically recognized as LFS- associated tumors, the occurrence of gastrointestinal neoplas...

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Autors principals: Masciari, Serena, Dewanwala, Akriti, Stoffel, Elena M, Lauwers, Gregory Y, Zheng, Hui, Achatz, Maria Isabel, Riegert-Johnson, Douglas, Foretova, Lenka, Silva, Edaise M., Digianni, Lisa, Verselis, Sigitas J, Schneider, Katherine, Li, Frederick P, Fraumeni, Joseph, Garber, Judy E, Syngal, Sapna
Format: Artigo
Idioma:Inglês
Publicat: 2011
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3595598/
https://ncbi.nlm.nih.gov/pubmed/21552135
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/GIM.0b013e31821628b6
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