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Alterations in Gene Expression in Mutant Amyloid Precursor Protein Transgenic Mice Lacking Niemann-Pick Type C1 Protein

Niemann-Pick type C (NPC) disease, a rare autosomal recessive disorder caused mostly by mutation in NPC1 gene, is pathologically characterized by the accumulation of free cholesterol in brain and other tissues. This is accompanied by gliosis and loss of neurons in selected brain regions, including t...

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Autori principali: Maulik, Mahua, Thinakaran, Gopal, Kar, Satyabrata
Natura: Artigo
Lingua:Inglês
Pubblicazione: Public Library of Science 2013
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3558508/
https://ncbi.nlm.nih.gov/pubmed/23382922
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0054605
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