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Complementation of arylsulfatase A in somatic hybrids of metachromatic leukodystrophy and multiple sulfatase deficiency disorder fibroblasts.

Metachromatic leukodystrophy and multiple sulfatase deficiency disorder are severe neurodegenerative diseases inherited as separate autosomal recessive traits. Arylsulfatase A (aryl-sulfate sulfohydrolase, EC 3.1.6.1) activity is deficient in both diseases but in multiple sulfatase deficiency disord...

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Sonraí Bibleagrafaíochta
Main Authors: Chang, P L, Davidson, R G
Formáid: Artigo
Teanga:Inglês
Foilsithe: 1980
Ábhair:
Rochtain Ar Líne:https://ncbi.nlm.nih.gov/pmc/articles/PMC350235/
https://ncbi.nlm.nih.gov/pubmed/6108562
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