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Compartmentalization of superoxide dismutase 1 (SOD1G93A) aggregates determines their toxicity

Neurodegenerative diseases constitute a class of illnesses marked by pathological protein aggregation in the brains of affected individuals. Although these disorders are invariably characterized by the degeneration of highly specific subpopulations of neurons, protein aggregation occurs in all cells...

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Autori principali: Weisberg, Sarah J., Lyakhovetsky, Roman, Werdiger, Ayelet-chen, Gitler, Aaron D., Soen, Yoav, Kaganovich, Daniel
Natura: Artigo
Lingua:Inglês
Pubblicazione: National Academy of Sciences 2012
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3465386/
https://ncbi.nlm.nih.gov/pubmed/22967507
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.1205829109
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