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mtDNA Deletion in an Iranian Infant with Pearson Marrow Syndrome

BACKGROUND: Pearson syndrome (PS) is a rare multisystem mitochondrial disorder of hematopoietic system, characterized by refractory sideroblastic anemia, pancytopenia, exocrine pancreatic insufficiency, and variable neurologic, hepatic, renal, and endocrine failure. CASE PRESENTATION: We describe a...

Disgrifiad llawn

Wedi'i Gadw mewn:
Manylion Llyfryddiaeth
Prif Awduron: Arzanian, Mohammad Taghi, Eghbali, Aziz, Karimzade, Parvaneh, Ahmadi, Mitra, Houshmand, Massoud, Rezaei, Nima
Fformat: Artigo
Iaith:Inglês
Cyhoeddwyd: Tehran University of Medical Sciences 2010
Pynciau:
Mynediad Ar-lein:https://ncbi.nlm.nih.gov/pmc/articles/PMC3445998/
https://ncbi.nlm.nih.gov/pubmed/23056691
Tagiau: Ychwanegu Tag
Dim Tagiau, Byddwch y cyntaf i dagio'r cofnod hwn!