Cargando...

Deletion of the huntingtin proline-rich region does not significantly affect normal huntingtin function in mice

The N-terminus of Huntingtin, the protein encoded by the Huntington’s disease gene, contains a stretch of polyglutamine residues that is expanded in Huntington’s disease. The polyglutamine stretch is flanked by two conserved protein domains in vertebrates: an N1-17 domain, and a proline-rich region...

Descripción completa

Guardado en:
Detalles Bibliográficos
Autores principales: Neveklovska, Michelle, Clabough, Erin B. D., Steffan, Joan S., Zeitlin, Scott O.
Formato: Artigo
Lenguaje:Inglês
Publicado: 2012
Materias:
Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC3432989/
https://ncbi.nlm.nih.gov/pubmed/22956985
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3233/JHD-2012-120016
Etiquetas: Agregar Etiqueta
Sin Etiquetas, Sea el primero en etiquetar este registro!