Wird geladen...

Update on the Phenotypic Spectrum of Lesch-Nyhan Disease and its Attenuated Variants

Congenital deficiency of the enzyme hypoxanthine-guanine phosphoribosyltransferase (HPRT) results in a spectrum of clinical phenotypes. All of these phenotypes are associated with marked overproduction of uric acid and related problems such as hyperuricemia, urate nephrolithiasis, tophi, and gout. T...

Ausführliche Beschreibung

Gespeichert in:
Bibliographische Detailangaben
Hauptverfasser: Torres, Rosa J., Puig, Juan G., Jinnah, Hyder A.
Format: Artigo
Sprache:Inglês
Veröffentlicht: 2012
Schlagworte:
Online Zugang:https://ncbi.nlm.nih.gov/pmc/articles/PMC3408650/
https://ncbi.nlm.nih.gov/pubmed/22198833
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s11926-011-0231-5
Tags: Tag hinzufügen
Keine Tags, Fügen Sie den ersten Tag hinzu!