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Update on the Phenotypic Spectrum of Lesch-Nyhan Disease and its Attenuated Variants

Congenital deficiency of the enzyme hypoxanthine-guanine phosphoribosyltransferase (HPRT) results in a spectrum of clinical phenotypes. All of these phenotypes are associated with marked overproduction of uric acid and related problems such as hyperuricemia, urate nephrolithiasis, tophi, and gout. T...

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Autori principali: Torres, Rosa J., Puig, Juan G., Jinnah, Hyder A.
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2012
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3408650/
https://ncbi.nlm.nih.gov/pubmed/22198833
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s11926-011-0231-5
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