Carregant...

Liver and Skin Histopathology in Adults with Acid Sphingomyelinase Deficiency (Niemann-Pick Disease Type B)

Acid sphingomyelinase deficiency (ASMD) is a lysosomal storage disorder characterized by the pathologic accumulation of sphingomyelin in multiple cells types, and occurs most prominently within the liver, spleen and lungs, leading to significant clinical disease. Seventeen ASMD patients underwent a...

Descripció completa

Guardat en:
Dades bibliogràfiques
Autors principals: Thurberg, Beth L., Wasserstein, Melissa P., Schiano, Thomas, O’Brien, Fanny, Richards, Susan, Cox, Gerald F., McGovern, Margaret M.
Format: Artigo
Idioma:Inglês
Publicat: 2012
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3396757/
https://ncbi.nlm.nih.gov/pubmed/22613999
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/PAS.0b013e31825793ff
Etiquetes: Afegir etiqueta
Sense etiquetes, Sigues el primer a etiquetar aquest registre!